What is infantile hemangioendothelioma?
Infantile hemangioendothelioma is a rare benign vascular tumor of the liver. We report a case of hepatic hemangioendothelioma in an 8- month-old female infant who presented with hepatomegaly and respiratory distress, which was successfully treated with oral prednisolone for six months.
What is a hamartoma liver?
Liver hamartoma is a rare type of benign tumor which usually occurs in the first few years of life. Although it is the second most common benign tumor in childhood, only about 100 cases have been reported in the English literature. Thus, it is extremely rare to encounter liver hamartoma in adults.
Is hemangioendothelioma malignant?
Background. Epithelioid hemangioendothelioma (EHE) is a rare malignant vascular neoplasm with increasing incidence. However, its clinical characteristics remain unclear due to its low incidence.
What is mesenchymal hamartoma?
Mesenchymal hamartoma is a rare, benign, developmental tumor of the liver, with occasional risk of malignancy. Histologically, it appears as a disordered arrangement of the mesenchyme, bile ducts, and hepatic parenchyma.
Is hepatoblastoma benign or malignant?
There are many types of benign and malignant (cancer) tumors that can occur in the liver. Hepatoblastoma is the most common malignant tumor of the liver and is typically diagnosed in children younger than 3 years old.
What is the treatment for hepatoblastoma?
Treatment for hepatoblastoma is aimed at removing (resecting) as much of the tumor as possible. Liver tissue can regenerate after a portion is removed. Most hepatoblastomas also require treatment with chemotherapy to shrink the tumor before surgery. This makes it easier and safer for the surgeon to remove the mass.
What is the survival rate from epithelioid hemangioendothelioma?
The prognosis of EHE is superior to that of angiosarcoma. In the present study, the 1-, 3-, and 5-year cumulative survival rates were 96.2%, 87.0%, and 75.3%, respectively.
What does an infantile hemangioendothelioma look like?
At unenhanced CT, infantile hemangioendothelioma usually manifests as a well-defined mass that is hypoattenuating relative to the normal liver parenchyma (, 8). In about 16%–40% of cases, the lesion is heterogeneous with central high-attenuation areas due to hemorrhage or calcifications (, 1,, 7,, 8).
What is the prognosis for hemangioendothelioma in humans?
The prognosis in each case depends on the type of hemangioendothelioma present, the risk of recurrence and whether the condition has metastasized (spread) to nearby tissues or other parts of the body.
When does hepatic epithelioid hemangioendothelioma ( Hehe ) peak incidence?
Hepatic epithelioid hemangioendothelioma (HEHE) is a rare, low to intermediate grade malignant hepatic vascular tumor. There may be a greater female incidence (with reported male-to-female ratio, 2:3), with peak incidence thought to be around the age of 30-40 years.
What kind of tumor is a kaposiform hemangioendothelioma?
Kaposiform hemangioendotheliomas grossly appear as infiltrating nodules/masses. Sizes vary from small nodules or plaques to massive infiltrating tumors. Lesions often show a purple/red coloration. Intra-thoracic and intra-abdominal lesions tend to be larger and more infiltrative than peripheral lesions 4,5.