What is the formula for PKU?
Phenyl-Free 1 is an iron-fortified infant formula & medical food powder that is free of the essential amino acid phenylalanine. It is specially designed for infants and toddlers with phenylketonuria (PKU).
What is Phenex formula?
Phenex Infant Formula is an Amino Acid-Modified Infant Formula With Iron. Phenex Infant Formula offers nutrition support of infants and toddlers with phenylketonuria (PKU). Phenex is Phenylalanine-free. Use Phenex Infant Formula under medical supervision.
What is the basic treatment for PKU phenylketonuria )?
PKU is treated by cutting back on protein to limit the intake of phenylalanine. If you or your child is diagnosed with moderate to severe PKU, you will need to adjust the diet to include special formulas and meals. These changes include a diet that is low in phenylalanine, while ensuring adequate protein intake.
What is the recommended management of a baby with PKU?
PKU is treated with a special diet. Newborn babies who test positive for PKU are placed on phenylalanine-free formula right away. As babies start to eat solid food, their diet will need to be restricted. This is because phenylalanine is found in many foods with protein.
How do you monitor PKU?
Your doctor can determine a safe amount through:
- Regular review of diet records, growth charts and blood levels of phenylalanine.
- Frequent blood tests that monitor phenylalanine levels as they change over time, especially during childhood growth spurts and pregnancy.
- Other tests that assess growth, development and health.
How do they test for PKU in newborns?
A PKU test is done a day or two after your baby’s birth. The test is done after your baby is 24 hours old and after your baby has ingested some protein in the diet to ensure accurate results. A nurse or lab technician collects a few drops of blood from your baby’s heel or the bend in your baby’s arm.
How much does PKU treatment cost?
On average, it costs $15,000 per person per year for treatment of PKU, including $5,000 for medical visits and $10,000 for medical food and formula. The costs of treating an individual with untreated PKU can be up to 13 times the cost of providing proper treatment.
What is the test used to detect phenylketonuria?
The Guthrie test, also called the PKU test, is a diagnostic tool to test infants for phenylketonuria a few days after birth. To administer the Guthrie test, doctors use Guthrie cards to collect capillary blood from an infant’s heel, and the cards are saved for later testing.
What do PKU babies drink?
If your baby has PKU, what kind of treatment do they need?
- Milk, cheese, ice cream and other dairy products.
- Eggs.
- Meat and poultry.
- Fish.
- Nuts, seeds, oats, rye, barley, gelatin.
- Beans.
- Food or drinks that contain aspartame. This is an artificial sweetener that has a lot of phenylalanine in it.