What is Landau-Kleffner syndrome?
Landau-Kleffner syndrome is a rare language disorder. It often happens in normally developing children, usually between 5 and 7 years of age, and is characterized by the slow or sudden loss of the ability to use or understand spoken language.
Is Landau-Kleffner syndrome autism?
Landau-Kleffner Syndrome It is twice as common in males than females and is often diagnosed in conjunction with autism. Initially, these individuals have a healthy, problem-free development with normal speech and vocabulary.
Is Landau-Kleffner syndrome a disability?
Some children with Landau-Kleffner syndrome may develop behavioral problems including hyperactivity, attention deficits, temper outbursts, impulsivity, and/or withdrawn behaviors. Some children with Landau Kleffner syndrome may also have intellectual disability .
What is Csws epilepsy?
Epilepsy with continuous spikes and waves during slow sleep (CSWS) is a rare neurological disease. CSWS is not an independent epilepsy syndrome but often accompanied by comprehensive damage of brain function and associated with various forms of epilepsy and neurodevelopmental problems.
Who discovered Landau Kleffner?
It is named after William Landau and Frank Kleffner, who characterized it in 1957 with a diagnosis of six children.
How is benign Rolandic epilepsy diagnosed?
A neurologist interprets the EEG. Children with benign rolandic epilepsy often have spikes on their EEG tracings that help make the diagnosis. Magnetic resonance imaging (MRI): This high-resolution scan of the brain is normal in children with benign rolandic epilepsy.
Can genetic seizures be cured?
There’s no cure for epilepsy, but the disorder can be managed with medications and other strategies.
How is Eses diagnosed?
Diagnosis of ESES is by demonstrating bilateral (rarely unilateral) continuous or near-continuous slow (1.5 to 3 Hz), diffuse, or bilateral, spike-wave discharges during NREM-sleep.
How rare is CSWS?
CSWS is a rare condition that affects 0.5-1.5% of children with epilepsy (in some series) and has a 3:2 male to female ratio. CSWS is an age-related epileptic encephalopathy in which the clinical features evolve over time.
What are sleep seizures?
Nocturnal seizures are seizures that happen while a person is asleep. They can cause unusual nighttime behavior, such as waking for no reason or urinating while sleeping, as well as jerking and shaking of the body. Nocturnal seizures are usually a type of seizure called a tonic-clonic seizure.
What do you need to know about Landau Kleffner syndrome?
Summary Summary. Landau-Kleffner syndrome (LKS) is a rare neurological syndrome characterized by the sudden or gradual development of aphasia (the inability to understand or express language) and recurrent seizures (epilepsy).
What kind of seizures do children with LKS have?
Seizures occur in 3 out of 4 children. They occur primarily during sleep and are infrequent. Seizures are usually focal motor seizures, but absence, atypical absence, and atonic seizures have been reported. LKS is also known as Progressive Epileptic Aphasia or Aphasia with Convulsive Disorder.
When does language impairment with epilepsy resolve?
Language impairment typically fluctuates. Seizures and EEG abnormality resolve with age in most cases, however residual language impairment is seen in the majority (>80%) and may be severe (especially if onset is earlier).
When do children with LKS lose their language skills?
LKS affects the parts of the brain that control comprehension and speech, typically affecting understanding rather than expression. The disorder usually occurs in children between the ages of 5 and 7 years. Typically, children with LKS develop normally but then lose their language skills for no apparent reason.