What does Fibroelastosis mean?
Medical Definition of fibroelastosis : a condition of the body or one of its organs (as the left ventricle of the heart) characterized by proliferation of fibroelastic tissue — see endocardial fibroelastosis.
What is a endocardial?
The endocardium is the innermost layer of the heart and lines the chambers and extends over projecting structures such as the valves, chordae tendineae, and papillary muscles.
What is endocardial Fibroelastosis?
Endocardial fibroelastosis (EFE) is a rare heart disorder that affects infants and children. It is characterized by a thickening within the muscular lining of the heart chambers due to an increase in the amount of supporting connective tissue (inelastic collagen) and elastic fibers.
What causes endomyocardial fibrosis?
A specific single etiology of endomyocardial fibrosis (EMF) has not been established. Suggested potential causes include the following : Infectious causes, such as parasites (eg, helminths) and protozoans (eg, toxoplasmosis, malaria) Inflammatory causes: Eosinophilia.
Can you live a long life with dilated cardiomyopathy?
“Some may have mild symptoms and live a fairly normal life, whereas others need to be treated more extensively. Treatment can range from medication to heart-transplant surgery. Some DCM patients may also need a pacemaker to control their heart rate, or an ICD to shock the heart back into rhythm if it stops.”
How does endocardial Fibroelastosis affect the heart?
The symptoms of endocardial fibroelastosis are related to the overgrowth of fibrous tissues causing abnormal enlargement of the heart (cardiac hypertrophy), especially the left ventricle. Impaired heart and lung function eventually lead to congestive heart failure.
What are endocardial cushions?
The endocardial cushions are two thicker areas that develop into the walls (septum) that divide the four chambers of the heart. They also form the mitral and tricuspid valves. These are the valves that separate the atria (top collecting chambers) from the ventricles (bottom pumping chambers).
What is the definition of endocardial fibroelastosis?
General Discussion. Endocardial fibroelastosis (EFE) is a rare heart disorder that affects infants and children. It is characterized by a thickening within the muscular lining of the heart chambers due to an increase in the amount of supporting connective tissue (inelastic collagen) and elastic fibers. The normal heart has four chambers.
How does endocardial fibroelastosis affect infants and children?
Endocardial fibroelastosis (EFE) is a rare heart disorder that affects infants and children. It is characterized by a thickening within the muscular lining of the heart chambers due to an increase in the amount of supporting connective tissue (inelastic collagen) and elastic fibers.
What’s the difference between EFE and endomyocardial fibrosis?
It should not be confused with endomyocardial fibrosis . EFE is characterized by a thickening of the innermost lining of the heart chambers (the endocardium) due to an increase in the amount of supporting connective tissue and elastic fibres.
What causes a thickening of the endocardium?
EFE is characterized by a thickening of the innermost lining of the heart chambers (the endocardium) due to an increase in the amount of supporting connective tissue and elastic fibres. It is an uncommon cause of unexplained heart failure in infants and children, and is one component of HEC syndrome.
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